Blood biomarkers recommended for diagnosing and monitoring IgG4-related disease. Considerations from the ERN ReCONNET and collaborating partners.

Jan 1, 2021·
MD PhD Luca Iaccarino
,
MD PhD Rosaria Talarico
,
MD Emanuele Bozzalla-Cassione
,
MD Gerd R. Burmester
,
MD PhD Emma L. Culver
,
MD Andrea Doria
,
MD Mikael Ebbo
,
PhDHyunSunJeon Md
,
M. Laar
,
M. Lanzillotta
,
MD Fernando Martinez-Valle
,
Priya Md
,
M. Monti
,
M. Nalli
,
MD Nicolas Schleinitz
,
M. Tincani
,
MD Emanuel Della-Torre
,
Prof Alexander
,
P. M. Hagen
· 0 min read
Abstract
Immunoglobulin G4 (IgG4)-related disease (IgG4-RD) is a chronic, clinically heterogenous fibroinflammatory condition, characterised by an accumulation of IgG4 secreting plasma cells in affected tissues and associated with increased serum IgG4 concentrations. Despite a growing recognition of the disease among clinicians from different specialties worldwide, its indolent nature, lack of a single diagnostic test and ability to mimic other malignant, infective and inflammatory conditions, makes the diagnosis challenging. As treatment options evolve, biomarkers correlating with disease activity, pr…
Type
Publication
Clinical and experimental rheumatology